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Gamma-Butyrobetaine Dioxygenase (BBOX1) Antibody
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Catalogue No: abx004452
Price:
US$203.00
(Size: 20 µl)
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BBOX1 Antibody is a Rabbit Polyclonal antibody against BBOX1. This gene encodes gamma butyrobetaine hydroxylase which catalyzes the formation of L-carnitine from gamma-butyrobetaine, the last step in the L-carnitine biosynthetic pathway. Carnitine is essential for the transport of activated fatty acids across the mitochondrial membrane during mitochondrial beta-oxidation.
Research Articles on Gamma-Butyrobetaine Dioxygenase (BBOX1)
| Target | Gamma-Butyrobetaine Dioxygenase (BBOX1) |
| Clonality | Polyclonal |
| Reactivity | Human, Mouse, Rat |
| Tested Applications | WB, IF/ICC |
| Host | Rabbit |
| Recommended dilutions | WB: 1/100 - 1/500, IF/ICC: 1/50 - 1/200. Optimal dilutions/concentrations should be determined by the end user. |
| Conjugation | Unconjugated |
| Immunogen | Recombinant fusion protein containing a sequence corresponding to amino acids 1-180 of human BBOX1. |
| Isotype | IgG |
| Form | Liquid |
| Purification | Purified by affinity chromatography. |
| Storage | Aliquot and store at -20°C. Avoid repeated freeze/thaw cycles. |
| UniProt Primary AC | O75936 (UniProt, ExPASy) |
| UniProt Secondary AC | B2R8L7, D3DQZ1, Q6IBJ2 |
| UniProt Entry Name | BODG_HUMAN |
| Gene Symbol | BBOX1 |
| GeneID | 8424 |
| OMIM | 603312 |
| NCBI Accession | NP_003977.1 |
| HGNC | 964 |
| KEGG | hsa:8424 |
| Ensembl | ENSG00000129151 |
| String | 9606.ENSP00000263182 |
| Molecular Weight | Calculated MW: 45 kDa Observed MW: 45 kDa |
| Buffer | PBS, pH 7.3, containing 0.02% sodium azide, 50% glycerol. |
| Concentration | > 0.2 mg/ml |
| Availability | Shipped within 5-10 working days. |
| Note | This product is for research use only. |