N-Acetylgalactosamine 6-Sulfatase (GALNS) Antibody

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Catalogue No: abx004181
Price: US$217.50
(Size: 20 µl)
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Western blot analysis of various lysates using GALNS Antibody at 1/1000 dilution. Secondary antibody: HRP-conjugated Goat anti-Rabbit IgG (H+L) at 1/10000 dilution. Lysates/proteins: 25 µg per lane. Blocking buffer: 3% nonfat dry milk in TBST. Exposure time: 15s.
N-Acetylgalactosamine 6-Sulfatase (GALNS) Antibody N-Acetylgalactosamine 6-Sulfatase (GALNS) Antibody N-Acetylgalactosamine 6-Sulfatase (GALNS) Antibody

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Datasheet SDS
GALNS Antibody is a Rabbit Polyclonal antibody against GALNS. This gene encodes N-acetylgalactosamine-6-sulfatase which is a lysosomal exohydrolase required for the degradation of the glycosaminoglycans, keratan sulfate, and chondroitin 6-sulfate. Sequence alterations including point, missense and nonsense mutations, as well as those that affect splicing, result in a deficiency of this enzyme. Deficiencies of this enzyme lead to Morquio A syndrome, a lysosomal storage disorder.

Target N-Acetylgalactosamine 6-Sulfatase (GALNS)
Clonality Polyclonal
Reactivity Human, Mouse, Rat
Tested Applications ELISA, WB, IF/ICC
Host Rabbit
Recommended dilutions ELISA: 1 µg/ml, WB: 1/500 - 1/2000, IF/ICC: 1/50 - 1/200. Optimal dilutions/concentrations should be determined by the end user.
Conjugation Unconjugated
Immunogen Recombinant fusion protein containing a sequence corresponding to amino acids 353-522 of human GALNS.
Isotype IgG
Form Liquid
Purification Purified by affinity chromatography.
Storage Aliquot and store at -20°C. Avoid repeated freeze/thaw cycles.
UniProt Primary AC P34059 (UniProt, ExPASy)
UniProt Secondary AC Q86VK3
UniProt Entry Name GALNS_HUMAN
Gene Symbol GALNS
GeneID 2588
OMIM 253000
NCBI Accession NP_000503.1
HGNC 4122
KEGG hsa:2588
Ensembl ENSG00000141012
String 9606.ENSP00000268695
Molecular Weight Calculated MW: 58 kDa
Observed MW: 55 kDa
Buffer PBS, pH 7.3, containing 0.02% sodium azide, 50% glycerol.
Concentration 2.32 mg/ml
Availability Shipped within 5-10 working days.
Note THIS PRODUCT IS FOR RESEARCH USE ONLY. NOT FOR USE IN DIAGNOSTIC, THERAPEUTIC OR COSMETIC PROCEDURES. NOT FOR HUMAN OR ANIMAL CONSUMPTION.
Research Articles on N-Acetylgalactosamine 6-Sulfatase (GALNS)
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