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Ornithine Carbamoyltransferase, Mitochondrial (OTC) Antibody
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Catalogue No: abx033070
Price:
US$326.25
(Size: 80 µl)
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OTC is a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia.
Research Articles on Ornithine Carbamoyltransferase, Mitochondrial (OTC)
| Target | Ornithine Carbamoyltransferase, Mitochondrial (OTC) |
| Clonality | Polyclonal |
| Reactivity | Human, Mouse, Rat |
| Tested Applications | ELISA, WB, IHC, FCM |
| Host | Rabbit |
| Recommended dilutions | WB: 1/2000, IHC-P: 1/10 - 1/50, FCM: 1/10 - 1/50. Not tested in IHC-F. Optimal dilutions/concentrations should be determined by the end user. |
| Conjugation | Unconjugated |
| Immunogen | KLH-conjugated synthetic peptide between 71-98 amino acids from the Central region of human OTC. |
| Isotype | IgG |
| Form | Liquid |
| Purification | Purified through a protein A column, followed by peptide affinity purification. |
| Storage | Aliquot and store at -20°C. Avoid repeated freeze/thaw cycles. |
| UniProt Primary AC | P00480 (UniProt, ExPASy) |
| UniProt Secondary AC | A8K9P2, D3DWB0, Q3KNR1, Q6B0I1, Q9NYJ5 |
| UniProt Entry Name | OTC_HUMAN |
| Gene Symbol | OTC |
| NCBI Accession | NP_000522.3 |
| KEGG | hsa:5009 |
| String | 9606.ENSP00000039007 |
| Molecular Weight | Calculated MW: 39.9 kDa |
| Buffer | PBS containing 0.09% sodium azide. |
| Specificity | Predicted to react with Cow, Pig and Sheep OTC. |
| Availability | Shipped within 5-10 working days. |
| Note | THIS PRODUCT IS FOR RESEARCH USE ONLY. NOT FOR USE IN DIAGNOSTIC, THERAPEUTIC OR COSMETIC PROCEDURES. NOT FOR HUMAN OR ANIMAL CONSUMPTION. |