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Propionyl-CoA Carboxylase Beta Chain, Mitochondrial (PCCB) Antibody
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Catalogue No: abx004148
Price:
US$217.50
(Size: 20 µl)
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PCCB Antibody is a Rabbit Polyclonal antibody against PCCB. The protein encoded by this gene is a subunit of the propionyl-CoA carboxylase (PCC) enzyme, which is involved in the catabolism of propionyl-CoA. PCC is a mitochondrial enzyme that probably acts as a dodecamer of six alpha subunits and six beta subunits. This gene encodes the beta subunit of PCC. Defects in this gene are a cause of propionic acidemia type II (PA-2). Multiple transcript variants encoding different isoforms have been found for this gene.
Research Articles on Propionyl-CoA Carboxylase Beta Chain, Mitochondrial (PCCB)
| Target | Propionyl-CoA Carboxylase Beta Chain, Mitochondrial (PCCB) |
| Clonality | Polyclonal |
| Reactivity | Human, Mouse |
| Tested Applications | ELISA, WB |
| Host | Rabbit |
| Recommended dilutions | ELISA: 1 µg/ml, WB: 1/500 - 1/2000. Optimal dilutions/concentrations should be determined by the end user. |
| Conjugation | Unconjugated |
| Immunogen | Recombinant fusion protein containing a sequence corresponding to amino acids 260-539 of human PCCB. |
| Isotype | IgG |
| Form | Liquid |
| Purification | Purified by affinity chromatography. |
| Storage | Aliquot and store at -20°C. Avoid repeated freeze/thaw cycles. |
| UniProt Primary AC | P05166 (UniProt, ExPASy) |
| UniProt Secondary AC | B7Z2Z4, Q16813, Q96CX0 |
| UniProt Entry Name | PCCB_HUMAN |
| Gene Symbol | PCCB |
| GeneID | 5096 |
| NCBI Accession | NP_000523.2 |
| KEGG | hsa:5096 |
| String | 9606.ENSP00000419027 |
| Molecular Weight | Calculated MW: 58 kDa Observed MW: 54 kDa |
| Buffer | PBS, pH 7.3, containing 0.02% sodium azide, 50% glycerol. |
| Concentration | > 0.2 mg/ml |
| Availability | Shipped within 5-10 working days. |
| Note | This product is for research use only. |